Description

This logic path provides recommendations for referral to genetic counseling for genetic/familial cancer risk assessment and consideration for genetic testing. These recommendations are provided independently of screening/surveillance recommendations, but are intending to act as an available stepping stone to in determining if the patient’s risk for colorectal cancer justifies intensified screening/surveillance initiation and intervals.

Mid-Level Flow Diagram

Family history ofinherited geneticsusceptibility tocolorectal cancer?Variant status known?Personal history ofsyndrome-relatedcancer diagnosedbefore age 50?Family history ofhereditarysyndrome-associatedcancer?1 or morefirst-degree relativediagnosed withhereditarysyndrome-associatedcancer diagnosedbefore age 50?3 or more relativeswith a hereditarysyndrome-associatedcancer?endRecommendation: Consider referralto genetic counseling for possiblegenetic testingRecommendation: Consider referralto genetic counseling forcomprehensive cancer riskassessment/genetic evaluationyesnoyesnoyesnoyesnoyesnoyesno

Semi-Structured Logic Statements

Inclusions

NameDescription
Patients eligible for screening
Patients for whom screening is clinically appropriate.
See 'Screening Eligible' logic path

Exclusions

None.

Events

NameDescription
Family history of inherited genetic susceptibility to colorectal cancer?
Variant status known?
Patient has been tested for the familial variant and a result is available.
Personal history of syndrome-related cancer diagnosed before age 50?
Patient has a history of a hereditary syndrome-related cancer diagnosed before age 50.
Family history of hereditary syndrome-associated cancer?
Patient has a family history of a cancer associated with a hereditary syndrome.
1 or more first-degree relative diagnosed with hereditary syndrome-associated cancer diagnosed before age 50?
Patient has at least one first-degree relative (mother, father, sibling or child) diagnosed with a hereditary cancer syndrome-related cancer before age 50.
FAMILY HISTORY includes DIAGNOSIS `Cancers Associated with Hereditary Cancer Syndromes Conferring Increased Risk of Colorectal Cancer` AND age at diagnosis <= 50 years
3 or more relatives with a hereditary syndrome-associated cancer?
Patient has 3 or more relatives (first-degree relatives - mother, father, sibling, or child - or second degree relatives - grandparents, half-siblings, first cousins, aunts and uncles, nieces and nephews)

Actions

Recommendation: Consider referral to genetic counseling for possible genetic testing
Description
RECOMMENDATION:
Cancer risk assessment and genetic counseling are highly recommended when genetic testing is offered, including consideration of the most appropriate tests to order.

Source: NCCN (2024)
Pseudocode
Recommendation: Consider referral to genetic counseling for comprehensive cancer risk assessment/genetic evaluation
Description
RECOMMENDATION:
Consider conducting a more comprehensive family history and/or referral to genetic counseling for a cancer risk assessment.

Source: ACG (2014), NCCN (2024)
Pseudocode

References

  • USMSTF (2014): Giardiello, F. M., et al. (2014). Guidelines on genetic evaluation and management of Lynch syndrome: A consensus statement by the US multi-society task force on colorectal cancer. American Journal of Gastroenterology, 109(8), 1159–1179. https://doi.org/10.1038/ajg.2014.186
  • NCCN (2.2024): NCCN Clinical Practice Guidelines in Oncology (NCCN Guidelines®) for Genetic/Familial High-Risk Assessment: Colorectal, Endometrial, and Gastric V.2.2024. https://www.nccn.org/professionals/physician_gls/pdf/genetics_ceg.pdf

Approved for Public Release, Distribution Unlimited.
Public Release Case Number 24-2711
Copyright ©2024 The MITRE Corporation. All rights reserved.